Urticaria Pigmentosa
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![HemePath_Urticaria14_Pigmentosa.jpg](/slides-13/slides/HemePath_Urticaria14_Pigmentosa.jpg)
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Maculopapular cutaneous mastocytosis (Urticaria pigmentosa) is the commonest form of cutaneous mastocytosis accounting for 80% of cases. The lesions measure 2-3 cm in diameter and are pruritic, erythematous or red-brown, round to oval macules, papules, or plaques. They are seen mainly on the trunk.