Comments:
This sharply circumscribed 3.5 cm pheochromocytoma presented in a 13 year old boy with von Hippel-Lindau disease. Susceptibility to pheochromocytoma is also seen in multiple endocrine neoplasia type 2 (MEN II), neurofibromatosis type 1, and pheochromocytoma-paraganglioma syndrome. Maher ER, Eng C. Hum Mol Genet 2002 Oct 1; 11(20):2347-54.return to Pheochromocytoma
