Myxopapillary ependymoma is a specific subtype of ependymomas that is seen almost exclusively in the conus medullaris and filum terminale of the spinal cord. The mean age at presentation is about 35 years. It is a slow-growing, WHO Grade I tumor with excellent prognosis when resected completely. Perivascular mucoid degeneration and dyscohesion produces papillary structures which are lined by cuboidal or columnar cells. There is abundant stromal mucin secreted by the tumor cells.